Pierre-Marie-Bamberger syndrome and solitary fibrous tumor: a rare association.

Pierre-Marie-Bamberger syndrome and solitary fibrous tumor: a rare association.

Asian Cardiovasc Thorac Ann. 2018 Jan 01;:218492318757042

Authors: Boyer-Duck E, Dajer-Fadel WL, Hernández-Arenas LÁ, Macías-Morales MP, Rodríguez-Gómez A, Romo-Aguirre C

Abstract
A solitary fibrous tumor originates in the pleura with variable degrees of invasion. Hypertrophic osteoarthropathy, known as Pierre-Marie-Bamberger syndrome, is characterized by clubbing of the fingers due to bone surface and soft tissue calcification, historically known as a bronchogenic carcinoma paraneoplastic syndrome; however, a few cases have been associated with solitary fibrous tumors. We describe the case of a 38-year-old woman who presented with clubbing of the fingers. Studies revealed an intrathoracic fibrous tumor that was successfully treated with improvement in symptoms.

PMID: 29378437 [PubMed - as supplied by publisher]

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