Noncirrhotic portal hypertension in necrobiotic xanthogranuloma associated with monoclonal gammopathy

Abstract

We report two cases of patients with necrobiotic xanthogranuloma (NXG) associated with monoclonal gammopathy. Besides cutaneous lesions, they both presented idiopathic non-cirrhotic portal hypertension (INCPH).

In 2007, a 65-year-old woman was referred for nodular eruption (Fig. 1 – A) located around the neck. Cervical skin biopsy showed normal epidermis and a layer of inflammatory elements on the reticular dermis.

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