The evolution of cerebrovascular changes in Köhlmeier-Degos disease: An 11-year follow-up case report.

The evolution of cerebrovascular changes in Köhlmeier-Degos disease: An 11-year follow-up case report.

J Clin Neurosci. 2017 Nov 24;:

Authors: Ye L, Lekgabe E, Tsui A, Gaillard F

Abstract
Köhlmeier-Degos disease is rare idiopathic vasculopathy, the exact pathogenesis of which remains unclear. Here, we review pertinent literatutre and present a case of a Köhlmeier-Degos disease with central nervous system involvement followed-up over 11 years with various neuroimaging modalities. Evolution of neurovascular and neuropathological changes over an extended time period has not been previously described.

PMID: 29239824 [PubMed - as supplied by publisher]

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