Σφακιανάκης Αλέξανδρος
ΩτοΡινοΛαρυγγολόγος
Αναπαύσεως 5 Άγιος Νικόλαος
Κρήτη 72100
00302841026182
00306932607174
alsfakia@gmail.com

Αρχειοθήκη ιστολογίου

! # Ola via Alexandros G.Sfakianakis on Inoreader

Η λίστα ιστολογίων μου

Τρίτη 20 Μαρτίου 2018

Oral manifestations of lipoid proteinosis in a 10-year-old female: A case report and literature update.

Related Articles

Oral manifestations of lipoid proteinosis in a 10-year-old female: A case report and literature update.

Oral Surg Oral Med Oral Pathol Oral Radiol. 2018 Feb 14;:

Authors: Lee KC, Peters SM, Ko YCK, Kunkle TC, Perrino MA, Yoon AJ, Philipone EM

Abstract
Lipoid proteinosis (LP) is a rare autosomal recessive disorder characterized by the deposition of amorphous hyaline material in the dermis and submucosal connective tissue. Here, we present a case of LP with significant oral, dermatologic, and neurologic manifestations occurring in a 10 year-old female of Asian descent. In addition to the more typical oral findings of restricted tongue movement and labial and buccal mucosal involvement, this case highlights an unusual pattern of gingival enlargement infrequently reported in the literature. As LP almost always involves the oral cavity, often before the onset of cutaneous lesions, it is important for dental providers to be familiar with the oral manifestations of this disease. Early detection and diagnosis of LP by the dental practitioner can help expedite proper multidisciplinary care and lead to significant reductions in patient morbidity and mortality.

PMID: 29548668 [PubMed - as supplied by publisher]



http://ift.tt/2u3Vvge

Δεν υπάρχουν σχόλια:

Δημοσίευση σχολίου

Αρχειοθήκη ιστολογίου