Clinical and surgical management of a congenital Type II split cord malformation presenting with progressive cranial neuropathies: case report.

Clinical and surgical management of a congenital Type II split cord malformation presenting with progressive cranial neuropathies: case report.

J Neurosurg Pediatr. 2016 Dec 23;:1-5

Authors: Maloney PR, Murphy ME, Sullan MJ, Van Abel KM, Cofer SA, Cheville JC, Wetjen NM

Abstract
Split cord malformation (SCM) is a rare abnormality of notochord development. The majority of cases occur in the thoracolumbar region, with more than 30 cases of cervical SCM reported. The clinical impact of SCMs involving the cervical cord is therefore largely unknown. In addition, the concomitant finding of brainstem involvement is presumably incompatible with life in the majority of patients, resulting in a paucity of data regarding this clinical scenario. In this paper the authors present the first case, to their knowledge, of an incomplete cervical SCM involving the brainstem and discuss its clinical impact, diagnosis, and management.

PMID: 28009225 [PubMed - as supplied by publisher]

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