Lymphomatoid granulomatosis with pulmonary and gastrointestinal involvement.

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Lymphomatoid granulomatosis with pulmonary and gastrointestinal involvement.

BMJ Case Rep. 2017 Feb 06;2017:

Authors: Kappen JH, van Zaanen HC, Snelder SM, van Tilburg AJ, Rudolphus A

Abstract
We present a rare case of grade II lymphomatoid granulomatosis (LYG) with pulmonary and gastrointestinal involvement. LYG is considered an Epstein-Barr virus-driven lymphoproliferative disorder that often presents with multiple nodular lesions in the lungs and sometimes involvement of skin and the central nervous system. Although the aetiology is unknown, it is associated with the use of immunosuppressives. Involvement of other organ systems is very rare. We successfully treated our patients with 6 cycles of R-CHOP and autologous stem cell transplantation with a major response at 20 months follow-up.

PMID: 28167690 [PubMed - indexed for MEDLINE]

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