Primary Hepatic Marginal zone Lymphoma: A rare coincidence

Publication date: Available online 8 January 2018
Source:Current Problems in Cancer
Author(s): Soumya Surath Panda, Manas Baisakh, Adyakinkar Panda, Hemlata Das
Primary hepatic lymphoma (PHL) is an extremely rare disease and is often misdiagnosed. The optimal therapy is still unclear and the outcomes are uncertain. Among PHLs, a primary hepatic low-grade marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue (MALT lymphoma) is still rarer. The present study reports the case of an elderly female diagnosed with primary hepatic lymphoma (MALT lymphoma) and treated with single agent rituximab. After 18 months, she had a progressive disease and developed Waldenstorms Macroglobulinemia concomitantly. To date, the patient has received two cycles of the RCOP (rituximab, cyclophosphamide, vincristine, and prednisone) regimen and patient′s condition is presently stable. This case is reported for its rarity and to convey the importance of the meticulous examination of the tissue. Diagnosis of this condition is important, because the disease is treatable.



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