Neurofibromas of the phrenic nerve: a case report and review of the literature.

Neurofibromas of the phrenic nerve: a case report and review of the literature.

World Neurosurg. 2015 Dec 30;

Authors: Ghali MG, Srinivasan VM, Jea A, Slopis JM, McCutcheon IE

Abstract
Phrenic neurofibromas are a rare pathological entity, with nine cases described in the English literature. They may occur in conjunction with or independently of neurofibromatosis type 1 (NF1). Phrenic neurofibromas post distinct therapeutic challenges compared to the more common phrenic schwannoma. We describe here a 14 year-old male with neurofibroma of the left phrenic nerve presenting as dextroposition of the heart after paralysis of the left hemidiaphragm allowed herniation of abdominal contents into the left hemithorax and displaced of the heart. Surgical resection of the tumor followed by diaphragmatic plication was performed to assess its degree of malignancy, reduce abdominal herniation, and improve lung capacity. The operation markedly improved his hemidiaphragmatic elevation. The spectrum of management options ranges from conservative surveillance to open thoracic surgery. Functional preservation of the phrenic nerve is technically challenging, and although phrenic neurofibromas often present with absent function that cannot be recovered, surgical intervention can be fruitful in restoring lung capacity through diaphragmatic reconstruction.

PMID: 26746336 [PubMed - as supplied by publisher]

from #PubMed 3 via ola Kala on Inoreader http://ift.tt/1SHfvbY
via IFTTT

from #Med Blogs by Alexandros G.Sfakianakis via Alexandros G.Sfakianakis on Inoreader http://ift.tt/1VWbCQe
via IFTTT