Multilevel spinal stabilization as a treatment for Hirayama disease: Report of an experience with 5 cases.

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Multilevel spinal stabilization as a treatment for Hirayama disease: Report of an experience with 5 cases.

World Neurosurg. 2016 Dec 05;:

Authors: Goel A, Dhar A, Shah A

Abstract
AIM: The authors analyze the role of multisegmental spinal instability in the pathogenesis of Hirayama's disease.
MATERIAL AND METHODS: During the period June 2014 to January 2016, the authors managed 5 cases having Hirayama disease. The patients were diagnosed on the basis of classical described radiological and clinical guidelines. All 5 patients were treated with multi-level cervical fixation that included fixation of the atlantoaxial joint in 4 patients, by adopting facetal fixation methods. No dural or bone decompression was done.The follow-up ranges from 7 to 26 months (average 17.6 months).
RESULTS: The most remarkable feature was an immediate postoperative and progressive improvement in the symptom of weakness, wasting and deformity of hands in all patients. The other remarkable feature was 'immediate' postoperative reduction in extradural mass in all patients and its complete disappearance in two patients.
CONCLUSIONS: From the observations, it appears that atlantoaxial and subaxial spinal instability plays a major role in the pathogenesis of Hirayama's disease.

PMID: 27931943 [PubMed - as supplied by publisher]

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