Sturge-Weber syndrome type 3 manifesting as 'Status migrainosus'.

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Sturge-Weber syndrome type 3 manifesting as 'Status migrainosus'.

BMJ Case Rep. 2016 Dec 19;2016:

Authors: Jordan PR, Iqbal M, Prasad M

Abstract
Sturge-Weber syndrome (SWS) is a rare neurocutaneous syndrome characterised by facial naevus and leptomeningeal angiomatosis resulting in neurological and ophthalmological complications. In its rare variant, SWS type 3, the clinical hallmark of facial naevus is absent which poses a diagnostic challenge. Here, we present an interesting case of SWS type 3 where a child presented twice with prolonged severe unilateral headache mimicking migraine status followed on both occasions with focal seizures. He developed a dense right-sided homonymous hemianopia, and an urgent brain MRI scan was performed which pointed towards the diagnosis of SWS type 3.

PMID: 27993821 [PubMed - indexed for MEDLINE]

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