Three Cases of Relapsing Polycondritis with Isolated Laryngotracheal Stenosis.

Three Cases of Relapsing Polycondritis with Isolated Laryngotracheal Stenosis.

Turk Arch Otorhinolaryngol. 2017 Jun;55(2):77-82

Authors: Taşlı H, Birkent H, Gerek M

Abstract
Relapsing polychondritis (RP) is a rare autoimmune and inflammatory disease, particularly characterized by recurrent inflammation of the hyaline cartilage. Laryngotracheal involvement in RP is the most serious complication that is observed in 50% of the patients and may lead to a life-threatening condition. The most common cause of death is laryngotracheal stenosis associated with lung infections or severe respiratory insufficiency that may be observed in 10%-50% of the patients. In this study, three RP patients comprising a child with isolated laryngotracheal stenosis have been presented.

PMID: 29392060 [PubMed]

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