Intracranial Epidural Metastases of Adrenal Pheochromocytoma: A Rare Entity.

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Intracranial Epidural Metastases of Adrenal Pheochromocytoma: A Rare Entity.

World Neurosurg. 2018 Mar 24;:

Authors: Boettcher LB, Abou-Al-Shaar H, Ravindra VM, Horn J, Palmer CA, Menacho ST

Abstract
Pheochromocytomas are uncommon neuroendocrine tumors of the adrenal medulla. Malignant behavior is seen in approximately 10% of these lesions, evidenced by distant metastasis to sites without chromaffin tissue. The authors report a rare case of intracranial epidural metastases of an adrenal pheochromocytoma in a 24-year-old man. The patient originally presented at the age of 10 years with adrenal pheochromocytoma and subsequently developed extensive metastatic bone and lung disease. He was monitored in the intervening years until recent imaging demonstrated an enlarging right parietal mass. Upon surgical resection of the parietal lesion, the tumor was highly vascularized and confined to the epidural space. To the best of the authors' knowledge, this is the first case of metastatic epidural spread of pheochromocytoma without concomitant subdural or intraparenchymal extension reported to date.

PMID: 29588244 [PubMed - as supplied by publisher]

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