[A very rare cause of peripheral precocious puberty in a girl: ovarian sex cord tumor with annular tubules].

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[A very rare cause of peripheral precocious puberty in a girl: ovarian sex cord tumor with annular tubules].

Arch Argent Pediatr. 2017 06 01;115(3):e179-e182

Authors: Sánchez Zahonero J, Ruiz Domínguez JA, Sánchez Zahonero S, López García MJ

Abstract
Sex cord tumor with annular tubules is an extremely uncommon gonadal stromal neoplasm. It represents 0.05-0.6% of all ovarian tumors, according to series. An unusual case is presented in a 6-year-old girl, detected as a result of an isosexual peripheral precocious puberty. The highlight of this case is that no mass attached to the ovary was found, but only a gonadal asymmetry without radiological signs of malignancy. After confirming the presence of tumoral cells by intraoperative biopsy, unilateral salpingo-oophorectomy with ipsilateral para-aortic and pelvic lymphadenectomy was performed. Afterwards, the evolution of the patient was favorable.

PMID: 28504506 [PubMed - indexed for MEDLINE]

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